| Diagnostic Grouping and Description | ICD-10-CM Code | |
|---|---|---|
| A. Central Nervous System | G90.1, Q00-Q07 | |
| A01. Anencephalus | Q00.0, Q00.1 | |
| A02. Spina Bifida w/o Anencephaly | ||
| A03. Hydrocephalus w/o Spina Bifida | Q03 | |
| A04. Encephalocele | Q01 | |
| A05. Microcephalus | Q02 | |
| B. Eye | Q10 - Q15, Q13.81, Q13.89 | |
| B01. Anopthalmos/Micropthalmos | Q11.0 - Q11.2 | |
| B02. Congenital Cataract | Q12.0 | |
| B03. Aniridia | Q13.1 | |
| C. Ear, Face and Neck | Q16-Q18 | |
| C01. Anotia/Microtia | Q16.0, Q17.2 | |
| D. Heart and Circulatory System | P29.3, P29.30, P29.38, Q20 - Q28, Q27.30 - Q27.39 |
|
| D01. Common Truncus | Q20.0 | |
| D02. Transposition of Great Vessels | Q20.2 Q20.3, Q20.5 | |
| D03. Tetralogy of Fallot | Q21.3 | |
| D04. Ventricular Septal Defect | Q21.0 | |
| D05. Atrial Septal Defect | Q21.1 | |
| D06. Endocardial Cushion Defect | Q21.1,Q21.2 | |
| D07. Pulmonary Valve Atresia and Stenosis | Q22.0, Q22.1 | |
| D08. Tricuspid Valve Atresia and Stenosis | Q22.4, Q22.6, Q22.8, Q22.9 | |
| D09. Ebstein's Anomaly | Q22.5 | |
| D10. Aortic Valve Stenosis | Q23.0 | |
| D11. Hypoplastic Left Heart Syndrome | Q23.4 | |
| D12. Patent Ductus Arteriosis | Q25.0 | |
| D13. Coarctation of Aorta | Q25.1 | |
| D14. Pulmonary Artery Anomalies | Q25.5, Q25.6, Q25.71, Q25.72, Q25.79 | |
| D15. Interrupted Aortic Arch | Q25.21, Q25.2, Q25.4 | |
| D16. Total Anomalous Pulmonary Venous Return | Q26.2 | |
| D17. Double Outlet Right Ventricle | Q20.1 | |
| D18. Single Ventricle | Q20.4 | |
| E. Respiratory System | Q30-Q34 | |
| E01. Lung Agenesis/Hypoplasia | Q33.2, Q33.3, Q33.6 | |
| E02. Choanal Atresia | Q30.0 | |
| F. Cleft Palate and Cleft Lip | Q35.1-Q37.9 | |
| F01. Cleft Palate | Q35.1. Q35.3, Q36.5, Q35.7, Q36.9 | |
| F02. Cleft Lip w and w/o Cleft Palate | Q36.0, Q36.1, Q36.9, Q37.1 - Q37.9 | |
| G. Upper Alimentary Canal/ Digestive System | Q38-Q37 | |
| G01. Esophageal Atresia/ Tracheoesophageal Fistula | Q39.0 - Q39.4 | |
| G02. Rectal and Large Intestinal Atresia/Stenosis | Q42.1 - Q42.3, Q42.8 - Q42.9 | |
| G03. Pyloric Stenosis | Q40.0 | |
| G04. Hirshsprung's Disease (congenital megacolon) | Q43.1, Q43.2 | |
| G05. Biliary Atresia | Q44.2, Q44.3 | |
| H. Genital and Urinary Systems | Q50.1 - Q64.9, Q50.01 - Q64.79, Q51.810 - Q51.828, Q53.111 - Q53.112, Q53.211 - Q53.212, Q53.23, R39.83 - R39.84 |
|
| H01. Renal Agenesis/Hypoplasia | Q60.0 - Q60.6 | |
| H02. Bladder Exstrophy | Q64.10, Q64.12, Q64.19 | |
| H03. Obstructive Genitourinary Defects | Q62.0, Q62.10 - Q62.12, Q62.2, Q62.31 - Q62.32, Q62.39, Q64.2, Q64.31 - Q64.33, Q64.39 |
|
| H04. Hypospadias & Epispadias | Q54.0 - Q54.3, Q54.8 - Q54.9 | |
| H05. Epispadias | Q64.0 | |
| I. Musculoskeletal System | Q65.1 - Q79.9, Q65.01 - Q79.59, Q71.811 - Q72.899, Q76.411 - Q76.429 |
|
| I01. Upper Limb Reduction Deformities | Q71.811 - Q71.813, Q71.819, Q71.891 - Q71.899, Q71.90 - Q71.93, Q71.00 - Q71.03, Q71.10 - Q71.13, Q71.20 - Q71.23, Q71.40 - Q71.43, Q71.50 - Q71.53, Q71.30 - Q71.33 |
|
| I02. Lower Limb Reduction Deformities | Q72.811 - Q72.813, Q72.819, Q72.891 - Q72.893, Q72.899, Q72.00 - Q72.03, Q72.90 - Q72.93, Q72.10 - Q72.13, Q72.50 - Q72.53, Q72.60 - Q72.63, Q72.30 - Q72.33, Q72.70 - Q72.73 |
|
| I03. Gastroschisis/Omphalocele | Q79.2-Q79.3 | |
| I03(a) Omphalocele | Q79.2 | |
| I03(b) Gastroschisis | Q79.3 | |
| I03(c) Other and Unspecified Abdominal Wall Anomalies | Q79.4, Q79.51 | |
| I04. Congenital Hip Dislocation | Q65.00,Q65.1-Q65.2 | |
| I05. Diaphragmatic Hernia | Q79.0-Q79.1 | |
| J. Integument | Q80-Q82, Q83.0 - Q83.8, Q84 | |
| K. Chromosomal Anomalies | Q90- Q99, Q93.81, Q93.88, Q93.89 |
|
| K01. Trisomy 13 | Q91.7 | |
| K02. Down Syndrome | Q90 | |
| K03. Trisomy 18 | Q91.0 - Q91.7 | |
| L. Other and Unspecified Congenital Anomalies | Q80-Q84, Q85.1 - Q99.2, Q78.71 - Q89.09, Q87.410 - Q87.418 |
|
| Diagnostic Grouping and Description | ICD-10-CM Code | |
|---|---|---|
| M. Infectious Conditions Occurring in the Perinatal Period | A50, A50.01 - A50.49, P35 - P37 |
|
| M01. Syphilis | A50.01 - A50.08, A50.1, A50.2, A50.9, A50.31, A50.40 - A50.49 | |
| M02. Other Infections | P35.0 - P35.8, P37 | |
| M03. Zika Virus Disease | A92.5 | |
| N. Familial/Congenital Neoplasms | Q85.00, Q85.01, Q85.02 | |
| O. Endocrine/Metabolic Disorders | C96.5, C96.6, D81, D81.810, D81.89, D82, D84.1, E00, E20.8, E20.9, E21.0 - E21.3, E23.0, E23.6, E25, E27.1, E27.2, E27.40, E27.49, E27.8, E29, E34.3, E70.0, E70.1, E70.20 - E70.30, E72, E70.310 - E70.339, E70.5 - E70.9, E71.0, E71.110 - E71.128, E71.19, E71.2, E71.310 - E71.318, E71.32, E71.39, E71.40-E71.43, E71.440, E71.448, E71.50, E71.53, E71.510 - E71.529, E71.540 - E71.548, E72.10 - E72.19, E70.40 - E70.49, E72.20 - E72.29, E72.3, E72.4, E72.50 - E72.59, E72.8, E72.9, E74.00 - E74.09, E74.20 - E74.29, E74.10 - E74.19, E74.31, E74.39, E74.4, E74.52, E74.53, E74.8, E74.9, E76.01 - E76.03, E76.1 - E76.9, E76.210, E76.211, E76.219, E76.22, E76.29, E78.0 - E78.6, E75.21, E75.22, E75.240 - E75.249, E77, E78.70. E78.79 - E78.89, E78.9, E80.3 - E80.7, E88.2, E88.89, C88.0, D47.2, D89.0, D89.1, E20.1, E83.10, E83.19, E83.30 - E83.39, E84.0 - E84.9, E84.11, E84.19, E88.01, E88.09, E80.0 - E80.7, E80.21, E80.29, E79.1, E79.8, E85.0 - E85.9, E88.40 - E88.49, E88.89, E88.9, H49.811 - H49.819, E85.81 - E85.89 | |
| P. Diseases of the Blood & Blood Forming Organs | D47.3, D55, D56, D57.1, D57.3, D57.00 - D57.02, D57.20, D57.40, D57.80, D57.211 - D57.219, D57.411 - D57.419, D57.811 - D57.819, D58.0, D58.1, D61.01, D61.09, D61.82, D65 - D67, D68, D68.31 - D68.32 | |
| Q. Other Diseases of the Central and Peripheral Nervous System | F84.0, E75.00 - E75.09, E75.10 - E75.19, E75.4, G11.0, G11.4, G12.0, G24.1, G31.9, G31.89, G40.401, G40.409, G40.411, G40.419, G51.0 - G51.9,G52.7, G60, G70.1 - G70.9, G70.00, G70.01, G70.80, G70.81, G71.0, G71.2, G71.11 - G71.19, G72.2, G72.3, G72.9, G73.3, G73.7, G80, G90.9, G91.2, G93.0, G94 | |
| R. Other Diseases of the Eye | H30.93, H35.23, H35.50 - H35.54, H47.22, H49.00 - H49.03, H49.10 - H49.13, H49.20 - H49.23, H49.30 - H49.33, H49.40 - H49.43, H49.881 - H49.889, H50.00 - H50.08, H50.011, H50.012, H50.021, H50.022, H50.031, H50.032, H50.041, H50.042, H50.10 - H50.18, H50.111, H50.112, H50.121, H50.122, H50.131, H50.132, H50.141, H50.142, H50.30 - H50.34, H50.311, H50.312, H50.331, H50.332, H50.40 - H50.43, H50.21, H50.22, H50.411, H50.412, H50.50 - H50.55, H50.60, H50.69, H50.611, H50.612, H50.811, H50.812, H50.89, H51.0 - H51.9, H51.11, H51.12, H51.20 - H51.23, H53.009, H53.019 - H53.039, H54.0 - H54.8, H54.0X33-H54.0X35, H54.0X43 - H54.0X45, H54.0X53 - H54.0X55, H54.10, H54.1131 - H54.1132, H54.1141 - H54.1142, H54.1213 - H54.1215, H54.1223 - H54.1225, H54.X11 - H54.X12, H54.X21 - H54.X22, H54.1151 - H54.1152, H54.40 - H54.42, H54.413A - H54.415A, H54.42A3 - H54.42A5, H54.50 - H54.52, H54.511A - H54.512A, H54.52A1 - H5452A2, H54.60 - H54.62, H54.7, H55.00 - H55.09, H55.81, H55.89 | |
| S. Hearing Deficiency | H90.0 - H90.8, H90.A11 - H90.A12, H90.11, H90.12, H90.A21 - H90.A22, H90.A31 - H90.A32, H90.41, H90.42, H90.71, H90.72, H91.8X1 - H91.8X9, H91.90 - H91.93, Q16.1 - Q16.9 | |
| T. Other Diseases of the Heart & Circulatory System | I42.1 - I42.8, I43, I44.0 - I44.7, I44.30, I44.39, I44.60, I44.69, I45.2 - I45.9, I45.10 - I45.81, I45.89, I47.1 - I47.9, I48.0, I48.1, I49.1- I49.2, I49.5 - I49.9, R00.1, I63.50, I66.9, I66.09, I66.19, I66.29, I66.30, I73,81, I82.0 | |
| U. Other Diseases of the Gastrointestinal System | K00, K01.0, K01.1, K31.4, K40.0, K40.00, K40.01, K40.10, K40.11, K40.20, K40.21, K40.3, K40.30, K40.31, K40.40, K40.41, K40.90, K40.91, K41.00, K41.01, K41.10, K41.11, K41.20, K41.21, K41.30, K41.31, K41.40, K41.41, K41.90, K41.91, K42.0 - K46.0, K42.1 - K46.1, K42.9 - K46.9, K43.19, K43.2, K43.7, K45.8, K56.2, K56.60, K60.3 - K60.5, K62.4, K63.2, M26.00 - N26.09, M26.10 - M26.19 | |
| V. Other Diseases of the Genital and Urinary Systems | N13.4, N13.5, N13.9, N28.82 - N28.89, N32.1, N32.2, N35.9, N36.0, N82 | |
| W. Other Fetal/Placental Anomalies | This grouping has been discontinued. | |
| X. Other Musculoskeletal System Diseases | M85.2 | |
| Y. Maternal Exposures Affecting Fetus | P00.2, P04.3, P04.8, P96.1, P04.41, P04.49, Q86.1 - Q86.8 | |
| Y01. Newborn Affected by Maternal Use of Alcohol | P04.3 | |
| Y02. Fetal Alcohol Syndrome | Q86.0 | |